display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, childbirth and the puerperium

excludes1: hemorrhage with coagulation defects (O45.-, O46.0-, O67.0, O72.3)


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, first trimester


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, second trimester


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, third trimester


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating pregnancy, unspecified trimester


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating childbirth


display: Other diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism complicating the puerperium


display: Endocrine, nutritional and metabolic diseases complicating pregnancy, childbirth and the puerperium

excludes2:
diabetes mellitus (O24.-)
malnutrition (O25.-)
postpartum thyroiditis (O90.5)


display: Obesity complicating pregnancy, childbirth, and the puerperium


display: Obesity complicating pregnancy, unspecified trimester


display: Obesity complicating pregnancy, first trimester


display: Obesity complicating pregnancy, second trimester


display: Obesity complicating pregnancy, third trimester


display: Other endocrine, nutritional and metabolic diseases complicating pregnancy, childbirth and the puerperium


display: Endocrine, nutritional and metabolic diseases complicating pregnancy, unspecified trimester


display: Endocrine, nutritional and metabolic diseases complicating pregnancy, first trimester


display: Endocrine, nutritional and metabolic diseases complicating pregnancy, second trimester


display: Endocrine, nutritional and metabolic diseases complicating pregnancy, third trimester


display: Endocrine, nutritional and metabolic diseases complicating childbirth


display: Endocrine, nutritional and metabolic diseases complicating the puerperium


display: Mental disorders and diseases of the nervous system complicating pregnancy, childbirth and the puerperium


display: Alcohol use complicating pregnancy, childbirth, and the puerperium


display: Alcohol use complicating pregnancy, unspecified trimester


display: Alcohol use complicating pregnancy, first trimester


display: Alcohol use complicating pregnancy, second trimester


display: Alcohol use complicating pregnancy, third trimester


display: Drug use complicating pregnancy, childbirth, and the puerperium


display: Drug use complicating pregnancy, unspecified trimester


display: Drug use complicating pregnancy, first trimester


display: Drug use complicating pregnancy, second trimester


display: Drug use complicating pregnancy, third trimester


display: Tobacco use disorder complicating pregnancy, childbirth, and the puerperium

names: Smoking complicating pregnancy, childbirth, and the puerperium


display: Smoking (tobacco) complicating pregnancy, unspecified trimester


display: Smoking (tobacco) complicating pregnancy, first trimester


display: Smoking (tobacco) complicating pregnancy, second trimester


display: Smoking (tobacco) complicating pregnancy, third trimester


display: Smoking (tobacco) complicating childbirth


display: Smoking (tobacco) complicating the puerperium


display: Other mental disorders complicating pregnancy, childbirth, and the puerperium

excludes2:
postpartum mood disturbance (O90.6)
postnatal psychosis (F53.1)
puerperal psychosis (F53.1)


display: Other mental disorders complicating pregnancy, unspecified trimester


display: Other mental disorders complicating pregnancy, first trimester


display: Other mental disorders complicating pregnancy, second trimester


display: Other mental disorders complicating pregnancy, third trimester


display: Other mental disorders complicating childbirth


display: Other mental disorders complicating the puerperium


display: Diseases of the nervous system complicating pregnancy, childbirth, and the puerperium

excludes2: pregnancy related peripheral neuritis (O26.8-)


display: Diseases of the nervous system complicating pregnancy, unspecified trimester


display: Diseases of the nervous system complicating pregnancy, first trimester


display: Diseases of the nervous system complicating pregnancy, second trimester


display: Diseases of the nervous system complicating pregnancy, third trimester


display: Diseases of the nervous system complicating childbirth


display: Diseases of the nervous system complicating the puerperium


display: Diseases of the circulatory system complicating pregnancy, childbirth and the puerperium

excludes2: venous complications and cerebrovenous sinus thrombosis in labor, childbirth and the puerperium (O87.-)

excludes2: venous complications and cerebrovenous sinus thrombosis in pregnancy (O22.-)


display: Diseases of the circulatory system complicating pregnancy


display: Diseases of the circulatory system complicating pregnancy, first trimester


display: Diseases of the circulatory system complicating pregnancy, second trimester


display: Diseases of the circulatory system complicating pregnancy, third trimester


display: Diseases of the circulatory system complicating pregnancy, unspecified trimester


display: Diseases of the circulatory system complicating childbirth


display: Diseases of the circulatory system complicating the puerperium


display: Diseases of the respiratory system complicating pregnancy, childbirth and the puerperium


display: Diseases of the respiratory system complicating pregnancy


display: Diseases of the respiratory system complicating pregnancy, first trimester


display: Diseases of the respiratory system complicating pregnancy, second trimester


display: Diseases of the respiratory system complicating pregnancy, third trimester


display: Diseases of the respiratory system complicating pregnancy, unspecified trimester


display: Diseases of the respiratory system complicating childbirth


display: Diseases of the respiratory system complicating the puerperium


display: Diseases of the digestive system complicating pregnancy, childbirth and the puerperium

excludes2: liver and biliary tract disorders in pregnancy, childbirth and the puerperium (O26.6-)


display: Diseases of the digestive system complicating pregnancy


display: Diseases of the digestive system complicating pregnancy, first trimester


display: Diseases of the digestive system complicating pregnancy, second trimester


display: Diseases of the digestive system complicating pregnancy, third trimester


display: Diseases of the digestive system complicating pregnancy, unspecified trimester


display: Diseases of the digestive system complicating childbirth


display: Diseases of the digestive system complicating the puerperium


display: Diseases of the skin and subcutaneous tissue complicating pregnancy, childbirth and the puerperium

excludes2: pruritic urticarial papules and plaques of pregnancy (PUPPP) (O26.86)


display: Diseases of the skin and subcutaneous tissue complicating pregnancy


display: Diseases of the skin and subcutaneous tissue complicating pregnancy, first trimester


display: Diseases of the skin and subcutaneous tissue complicating pregnancy, second trimester


display: Diseases of the skin and subcutaneous tissue complicating pregnancy, third trimester


display: Diseases of the skin and subcutaneous tissue complicating pregnancy, unspecified trimester


display: Diseases of the skin and subcutaneous tissue complicating childbirth


display: Diseases of the skin and subcutaneous tissue complicating the puerperium


display: Other specified diseases and conditions complicating pregnancy, childbirth and the puerperium

excludes2: genitourinary infections in pregnancy (O23.-)

excludes2: infection of genitourinary tract following delivery (O86.1-O86.3)

excludes2: malignant neoplasm complicating pregnancy, childbirth and the puerperium (O9A.1-)

excludes2: maternal care for known or suspected abnormality of maternal pelvic organs (O34.-)

excludes2: traumatic injuries in pregnancy (O9A.2-)

names: Conditions in D00-D48, H00-H95, M00-N99, and Q00-Q99


display: Abnormal glucose complicating pregnancy, childbirth and the puerperium


display: Abnormal glucose complicating childbirth


display: Abnormal glucose complicating the puerperium


display: Streptococcus B carrier state complicating pregnancy, childbirth and the puerperium

excludes1: Carrier of streptococcus group B (GBS) in a nonpregnant woman (Z22.330)


display: Streptococcus B carrier state complicating pregnancy


display: Streptococcus B carrier state complicating childbirth


display: Streptococcus B carrier state complicating the puerperium


display: Other infection carrier state complicating pregnancy, childbirth and the puerperium


display: Other infection carrier state complicating pregnancy


display: Other infection carrier state complicating childbirth


display: Other infection carrier state complicating the puerperium


display: Bariatric surgery status complicating pregnancy, childbirth and the puerperium

names: Gastric banding status complicating pregnancy, childbirth and the puerperium

names: Gastric bypass status for obesity complicating pregnancy, childbirth and the puerperium

names: Obesity surgery status complicating pregnancy, childbirth and the puerperium


display: Bariatric surgery status complicating pregnancy, unspecified trimester


display: Bariatric surgery status complicating pregnancy, first trimester


display: Bariatric surgery status complicating pregnancy, second trimester


display: Bariatric surgery status complicating pregnancy, third trimester


display: Bariatric surgery status complicating childbirth


display: Bariatric surgery status complicating the puerperium


display: Other specified diseases and conditions complicating pregnancy, childbirth and the puerperium


display: Maternal malignant neoplasms, traumatic injuries and abuse classifiable elsewhere but complicating pregnancy, childbirth and the puerperium


display: Malignant neoplasm complicating pregnancy, childbirth and the puerperium

excludes2: maternal care for benign tumor of corpus uteri (O34.1-)

excludes2: maternal care for benign tumor of cervix (O34.4-)


display: Malignant neoplasm complicating pregnancy


display: Malignant neoplasm complicating pregnancy, first trimester


display: Malignant neoplasm complicating pregnancy, second trimester


display: Malignant neoplasm complicating pregnancy, third trimester


display: Malignant neoplasm complicating pregnancy, unspecified trimester


display: Malignant neoplasm complicating childbirth


display: Malignant neoplasm complicating the puerperium


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy, childbirth and the puerperium

excludes2: physical, sexual and psychological abuse complicating pregnancy, childbirth and the puerperium (O9A.3-, O9A.4-, O9A.5-)

names: Conditions in S00-T88, except T74 and T76


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy, first trimester


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy, second trimester


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy, third trimester


display: Injury, poisoning and certain other consequences of external causes complicating pregnancy, unspecified trimester


display: Injury, poisoning and certain other consequences of external causes complicating childbirth


display: Injury, poisoning and certain other consequences of external causes complicating the puerperium


display: Physical abuse complicating pregnancy, childbirth and the puerperium

excludes2: sexual abuse complicating pregnancy, childbirth and the puerperium (O9A.4)


display: Physical abuse complicating pregnancy, first trimester


display: Physical abuse complicating pregnancy, second trimester


display: Physical abuse complicating pregnancy, third trimester


display: Physical abuse complicating pregnancy, unspecified trimester


display: Physical abuse complicating the puerperium


display: Sexual abuse complicating pregnancy, childbirth and the puerperium


display: Sexual abuse complicating pregnancy, first trimester


display: Sexual abuse complicating pregnancy, second trimester


display: Sexual abuse complicating pregnancy, third trimester


display: Sexual abuse complicating pregnancy, unspecified trimester


display: Sexual abuse complicating the puerperium


display: Psychological abuse complicating pregnancy, childbirth and the puerperium


display: Psychological abuse complicating pregnancy


display: Psychological abuse complicating pregnancy, first trimester


display: Psychological abuse complicating pregnancy, second trimester


display: Psychological abuse complicating pregnancy, third trimester


display: Psychological abuse complicating pregnancy, unspecified trimester


display: Psychological abuse complicating childbirth


display: Psychological abuse complicating the puerperium


display: Newborn affected by maternal conditions that may be unrelated to present pregnancy

excludes2: encounter for observation of newborn for suspected diseases and conditions ruled out (Z05.-)

excludes2: newborn affected by maternal complications of pregnancy (P01.-)

excludes2: newborn affected by maternal endocrine and metabolic disorders (P70-P74)

excludes2: newborn affected by noxious substances transmitted via placenta or breast milk (P04.-)


display: Newborn affected by maternal hypertensive disorders

names: Newborn affected by maternal conditions classifiable to O10-O11, O13-O16


display: Newborn affected by maternal renal and urinary tract diseases

names: Newborn affected by maternal conditions classifiable to N00-N39


display: Newborn affected by maternal infectious and parasitic diseases

excludes1: maternal genital tract or other localized infections (P00.8)

excludes2: infections specific to the perinatal period (P35-P39)

names: Newborn affected by maternal infectious disease classifiable to A00-B99, J09 and J10


display: Newborn affected by other maternal circulatory and respiratory diseases

names: Newborn affected by maternal conditions classifiable to I00-I99, J00-J99, Q20-Q34 and not included in P00.0, P00.2


display: Newborn affected by maternal nutritional disorders

names: Newborn affected by maternal disorders classifiable to E40-E64


display: Newborn affected by maternal injury

names: Newborn affected by maternal conditions classifiable to O9A.2-


display: Newborn affected by surgical procedure on mother

excludes1: Cesarean delivery for present delivery (P03.4)

excludes1: damage to placenta from amniocentesis, Cesarean delivery or surgical induction (P02.1)

excludes1: previous surgery to uterus or pelvic organs (P03.89)

excludes2: newborn affected by complication of (fetal) intrauterine procedure (P96.5)


display: Newborn affected by other medical procedures on mother, not elsewhere classified

excludes1: damage to placenta from amniocentesis, cesarean delivery or surgical induction (P02.1)

excludes1: newborn affected by other complications of labor and delivery (P03.-)


display: Newborn affected by other maternal conditions


display: Newborn affected by periodontal disease in mother


names: Newborn affected by conditions classifiable to T80-T88

names: Newborn affected by maternal genital tract or other localized infections

names: Newborn affected by maternal systemic lupus erythematosus


display: Newborn affected by unspecified maternal condition


display: Newborn affected by maternal complications of pregnancy


display: Newborn affected by premature rupture of membranes


display: Newborn affected by oligohydramnios

excludes1: oligohydramnios due to premature rupture of membranes (P01.1)


display: Newborn affected by multiple pregnancy

names:
Newborn affected by triplet (pregnancy)
Newborn affected by twin (pregnancy)


display: Newborn affected by malpresentation before labor

names: Newborn affected by breech presentation before labor

names: Newborn affected by external version before labor

names: Newborn affected by face presentation before labor

names: Newborn affected by transverse lie before labor

names: Newborn affected by unstable lie before labor


display: Newborn affected by other maternal complications of pregnancy


display: Newborn affected by maternal complication of pregnancy, unspecified


display: Newborn affected by complications of placenta, cord and membranes


display: Newborn affected by other forms of placental separation and hemorrhage

names: Newborn affected by accidental hemorrhage

names: Newborn affected by antepartum hemorrhage

names: Newborn affected by damage to placenta from amniocentesis, cesarean delivery or surgical induction

names: Newborn affected by premature separation of placenta


display: Newborn affected by other and unspecified morphological and functional abnormalities of placenta


display: Newborn affected by unspecified morphological and functional abnormalities of placenta


display: Newborn affected by other morphological and functional abnormalities of placenta

names: Newborn affected by placental dysfunction

names: Newborn affected by placental infarction

names: Newborn affected by placental insufficiency


display: Newborn affected by placental transfusion syndromes

names: Newborn affected by placental and cord abnormalities resulting in twin-to-twin or other transplacental transfusion


display: Newborn affected by other compression of umbilical cord

names: Newborn affected by umbilical cord (tightly) around neck

names: Newborn affected by entanglement of umbilical cord

names: Newborn affected by knot in umbilical cord


display: Newborn affected by other and unspecified conditions of umbilical cord


display: Newborn affected by unspecified conditions of umbilical cord


display: Newborn affected by other conditions of umbilical cord

excludes1: newborn affected by single umbilical artery (Q27.0)

names: Newborn affected by short umbilical cord


display: Newborn affected by fetal inflammatory response syndrome


display: Newborn affected by other conditions from chorioamnionitis

names:
Newborn affected by amnionitis
Newborn affected by membranitis
Newborn affected by placentitis


display: Newborn affected by other abnormalities of membranes


display: Newborn affected by abnormality of membranes, unspecified


display: Newborn affected by other complications of labor and delivery


display: Newborn affected by breech delivery and extraction


display: Newborn affected by other malpresentation, malposition and disproportion during labor and delivery

names: Newborn affected by conditions classifiable to O64-O66

names: Newborn affected by persistent occipitoposterior


display: Newborn affected by delivery by vacuum extractor [ventouse]


display: Newborn affected by precipitate delivery


display: Newborn affected by abnormal uterine contractions

names: Newborn affected by conditions classifiable to O62.-, except O62.3


display: Newborn affected by other specified complications of labor and delivery


display: Newborn affected by abnormality in fetal (intrauterine) heart rate or rhythm


display: Newborn affected by abnormality in fetal (intrauterine) heart rate or rhythm before the onset of labor


display: Newborn affected by abnormality in fetal (intrauterine) heart rate or rhythm during labor


display: Newborn affected by abnormality in fetal (intrauterine) heart rate or rhythm, unspecified as to time of onset


display: Meconium passage during delivery

excludes1:
meconium aspiration (P24.00, P24.01)
meconium staining (P96.83)


names: Newborn affected by abnormality of maternal soft tissues

names: Newborn affected by conditions classifiable to O60-O75 and by procedures used in labor and delivery not included in P02.- and P03.0-P03.6


display: Newborn affected by complication of labor and delivery, unspecified


display: Newborn affected by noxious substances transmitted via placenta or breast milk

excludes2: neonatal jaundice from excessive hemolysis due to drugs or toxins transmitted from mother (P58.4)

excludes2: newborn in contact with and (suspected) exposures hazardous to health not transmitted via placenta or breast milk (Z77.-)

names: nonteratogenic effects of substances transmitted via placenta


display: Newborn affected by maternal anesthesia and analgesia in pregnancy, labor and delivery

excludes2: newborn affected by other maternal medication (P04.1-)

names: Newborn affected by reactions and intoxications from maternal opiates and tranquilizers administered for procedures during pregnancy or labor and delivery


display: Newborn affected by other maternal medication

excludes1:
dysmorphism due to warfarin (Q86.2)
fetal hydantoin syndrome (Q86.1)

excludes2: maternal anesthesia and analgesia in pregnancy, labor and delivery (P04.0)

excludes2: maternal use of drugs of addiction (P04.4-)


display: Newborn affected by maternal antineoplastic chemotherapy


display: Newborn affected by maternal cytotoxic drugs


display: Newborn affected by maternal use of anticonvulsants


display: Newborn affected by maternal use of opiates


display: Newborn affected by maternal use of antidepressants


display: Newborn affected by maternal use of amphetamines


display: Newborn affected by maternal use of sedative-hypnotics


display: Newborn affected by maternal use of anxiolytics


display: Newborn affected by maternal use of unspecified medication


display: Newborn affected by maternal use of tobacco

excludes2: newborn exposure to environmental tobacco smoke (P96.81)

names: Newborn affected by exposure in utero to tobacco smoke


display: Newborn affected by maternal use of alcohol


display: Newborn affected by maternal use of drugs of addiction


display: Newborn affected by maternal use of unspecified drugs of addiction


display: Newborn affected by maternal use of cocaine


display: Newborn affected by maternal use of hallucinogens


display: Newborn affected by maternal use of other drugs of addiction

excludes2: newborn affected by maternal anesthesia and analgesia (P04.0)

excludes2: withdrawal symptoms from maternal use of drugs of addiction (P96.1)


display: Newborn affected by maternal use of nutritional chemical substances


display: Newborn affected by maternal exposure to environmental chemical substances


display: Newborn affected by other maternal noxious substances


display: Newborn affected by maternal use of cannabis


display: Newborn affected by maternal noxious substance, unspecified


display: Disorders of newborn related to slow fetal growth and fetal malnutrition


display: Newborn light for gestational age

names: Weight below but length above 10th percentile for gestational age


display: Newborn light for gestational age, unspecified weight


display: Newborn light for gestational age, less than 500 grams


display: Newborn light for gestational age, 500-749 grams


display: Newborn light for gestational age, 750-999 grams


display: Newborn light for gestational age, 1000-1249 grams


display: Newborn light for gestational age, 1250-1499 grams


display: Newborn light for gestational age, 1500-1749 grams


display: Newborn light for gestational age, 1750-1999 grams


display: Newborn light for gestational age, 2000-2499 grams


display: Newborn light for gestational age, 2500 grams and over

names: Newborn light for gestational age, other


display: Newborn small for gestational age

names: Weight and length below 10th percentile for gestational age


display: Newborn small for gestational age, unspecified weight


display: Newborn small for gestational age, less than 500 grams


display: Newborn small for gestational age, 500-749 grams


display: Newborn small for gestational age, 750-999 grams


display: Newborn small for gestational age, 1000-1249 grams


display: Newborn small for gestational age, 1250-1499 grams


display: Newborn small for gestational age, 1500-1749 grams


display: Newborn small for gestational age, 1750-1999 grams


display: Newborn small for gestational age, 2000-2499 grams


display: Newborn small for gestational age, other

names: Newborn small for gestational age, 2500 grams and over


display: Newborn affected by fetal (intrauterine) malnutrition not light or small for gestational age

excludes1: newborn affected by fetal malnutrition with light for gestational age (P05.0-)

excludes1: newborn affected by fetal malnutrition with small for gestational age (P05.1-)

names: Infant, not light or small for gestational age, showing signs of fetal malnutrition, such as dry, peeling skin and loss of subcutaneous tissue


display: Newborn affected by slow intrauterine growth, unspecified

names: Newborn affected by fetal growth retardation NOS


display: Disorders of newborn related to short gestation and low birth weight, not elsewhere classified

names: the listed conditions, without further specification, as the cause of morbidity or additional care, in newborn


display: Extremely low birth weight newborn

excludes1: low birth weight due to slow fetal growth and fetal malnutrition (P05.-)


display: Extremely low birth weight newborn, unspecified weight


display: Extremely low birth weight newborn, less than 500 grams


display: Extremely low birth weight newborn, 500-749 grams


display: Extremely low birth weight newborn, 750-999 grams


display: Other low birth weight newborn


display: Other low birth weight newborn, unspecified weight


display: Other low birth weight newborn, 1000-1249 grams


display: Other low birth weight newborn, 1250-1499 grams


display: Other low birth weight newborn, 1500-1749 grams


display: Other low birth weight newborn, 1750-1999 grams


display: Other low birth weight newborn, 2000-2499 grams


display: Extreme immaturity of newborn

names: Less than 28 completed weeks (less than 196 completed days) of gestation.


display: Extreme immaturity of newborn, unspecified weeks of gestation

names: Gestational age less than 28 completed weeks NOS


display: Extreme immaturity of newborn, gestational age less than 23 completed weeks

names: Extreme immaturity of newborn, gestational age less than 23 weeks, 0 days


display: Extreme immaturity of newborn, gestational age 23 completed weeks

names: Extreme immaturity of newborn, gestational age 23 weeks, 0 days through 23 weeks, 6 days


display: Extreme immaturity of newborn, gestational age 24 completed weeks

names: Extreme immaturity of newborn, gestational age 24 weeks, 0 days through 24 weeks, 6 days


display: Extreme immaturity of newborn, gestational age 25 completed weeks

names: Extreme immaturity of newborn, gestational age 25 weeks, 0 days through 25 weeks, 6 days


display: Extreme immaturity of newborn, gestational age 26 completed weeks

names: Extreme immaturity of newborn, gestational age 26 weeks, 0 days through 26 weeks, 6 days


display: Extreme immaturity of newborn, gestational age 27 completed weeks

names: Extreme immaturity of newborn, gestational age 27 weeks, 0 days through 27 weeks, 6 days


display: Preterm [premature] newborn [other]

names: 28 completed weeks or more but less than 37 completed weeks (196 completed days but less than 259 completed days) of gestation.


display: Preterm newborn, unspecified weeks of gestation


display: Preterm newborn, gestational age 28 completed weeks

names: Preterm newborn, gestational age 28 weeks, 0 days through 28 weeks, 6 days


display: Preterm newborn, gestational age 29 completed weeks

names: Preterm newborn, gestational age 29 weeks, 0 days through 29 weeks, 6 days


display: Preterm newborn, gestational age 30 completed weeks

names: Preterm newborn, gestational age 30 weeks, 0 days through 30 weeks, 6 days


display: Preterm newborn, gestational age 31 completed weeks

names: Preterm newborn, gestational age 31 weeks, 0 days through 31 weeks, 6 days


display: Preterm newborn, gestational age 32 completed weeks

names: Preterm newborn, gestational age 32 weeks, 0 days through 32 weeks, 6 days


display: Preterm newborn, gestational age 33 completed weeks

names: Preterm newborn, gestational age 33 weeks, 0 days through 33 weeks, 6 days


display: Preterm newborn, gestational age 34 completed weeks

names: Preterm newborn, gestational age 34 weeks, 0 days through 34 weeks, 6 days


display: Preterm newborn, gestational age 35 completed weeks

names: Preterm newborn, gestational age 35 weeks, 0 days through 35 weeks, 6 days


display: Preterm newborn, gestational age 36 completed weeks

names: Preterm newborn, gestational age 36 weeks, 0 days through 36 weeks, 6 days


display: Disorders of newborn related to long gestation and high birth weight

names: the listed conditions, without further specification, as causes of morbidity or additional care, in newborn


display: Exceptionally large newborn baby

excludes1: syndrome of infant of diabetic mother (P70.1)

excludes1: syndrome of infant of mother with gestational diabetes (P70.0)

names: Usually implies a birth weight of 4500 g. or more


display: Other heavy for gestational age newborn

excludes1: newborn with a birth weight of 4500 or more (P08.0)

excludes1: syndrome of infant of mother with gestational diabetes (P70.0).

names: Other newborn heavy- or large-for-dates regardless of period of gestation

names: Usually implies a birth weight of 4000 g. to 4499 g.


display: Late newborn, not heavy for gestational age


display: Post-term newborn

names: Newborn with gestation period over 40 completed weeks to 42 completed weeks


display: Prolonged gestation of newborn

names: Newborn with gestation period over 42 completed weeks (294 days or more), not heavy- or large-for-dates.


display: Abnormal findings on neonatal screening

excludes2: nonspecific serologic evidence of human immunodeficiency virus [HIV] (R75)


display: Intracranial laceration and hemorrhage due to birth injury

excludes1: intracranial hemorrhage of newborn NOS (P52.9)

excludes1: intracranial hemorrhage of newborn due to anoxia or hypoxia (P52.-)

excludes1: nontraumatic intracranial hemorrhage of newborn (P52.-)


display: Subdural hemorrhage due to birth injury

excludes1: subdural hemorrhage accompanying tentorial tear (P10.4)

names: Subdural hematoma (localized) due to birth injury


display: Intraventricular hemorrhage due to birth injury


display: Subarachnoid hemorrhage due to birth injury


display: Other intracranial lacerations and hemorrhages due to birth injury


display: Unspecified intracranial laceration and hemorrhage due to birth injury


display: Other birth injuries to central nervous system


display: Other specified brain damage due to birth injury


display: Unspecified brain damage due to birth injury


display: Birth injury to central nervous system, unspecified


display: Chignon (from vacuum extraction) due to birth injury


display: Epicranial subaponeurotic hemorrhage due to birth injury


display: Injury of scalp of newborn due to monitoring equipment

names: Scalp clip (electrode) injury of newborn


display: Fracture of clavicle due to birth injury


display: Birth injuries to other parts of skeleton


display: Birth injury to peripheral nervous system


display: Phrenic nerve paralysis due to birth injury


display: Birth injuries to other parts of peripheral nervous system


display: Birth injury to peripheral nervous system, unspecified


display: Sternomastoid injury due to birth injury


display: Birth injury to eye

names: Subconjunctival hemorrhage due to birth injury


display: Subcutaneous fat necrosis due to birth injury


display: Metabolic acidemia in newborn first noted before onset of labor


display: Metabolic acidemia in newborn first noted during labor


display: Respiratory distress of newborn

excludes1: respiratory failure of newborn NOS (P28.5)


display: Respiratory distress syndrome of newborn

names: Cardiorespiratory distress syndrome of newborn

names: Idiopathic respiratory distress syndrome [IRDS or RDS] of newborn


display: Transient tachypnea of newborn

names:
Idiopathic tachypnea of newborn
Respiratory distress syndrome, type II
Wet lung syndrome


display: Respiratory distress of newborn, unspecified


display: Congenital pneumonia

excludes1: neonatal pneumonia resulting from aspiration (P24.-)

names: infective pneumonia acquired in utero or during birth


display: Congenital pneumonia due to staphylococcus


display: Congenital pneumonia due to streptococcus, group B


display: Congenital pneumonia due to Escherichia coli


display: Congenital pneumonia due to other bacterial agents

names: Congenital pneumonia due to Hemophilus influenzae

names: Congenital pneumonia due to Klebsiella pneumoniae

names: Congenital pneumonia due to Streptococcus, except group B


display: Congenital pneumonia due to other organisms


display: Meconium aspiration

excludes1: meconium passage (without aspiration) during delivery (P03.82 )


display: Meconium aspiration without respiratory symptoms


display: Meconium aspiration with respiratory symptoms

names:
Meconium aspiration pneumonia
Meconium aspiration pneumonitis
Meconium aspiration syndrome NOS


display: Neonatal aspiration of (clear) amniotic fluid and mucus


display: Neonatal aspiration of (clear) amniotic fluid and mucus without respiratory symptoms

names: Neonatal aspiration of amniotic fluid and mucus NOS


display: Neonatal aspiration of (clear) amniotic fluid and mucus with respiratory symptoms

names: Neonatal aspiration of amniotic fluid and mucus with pneumonia

names: Neonatal aspiration of amniotic fluid and mucus with pneumonitis


display: Neonatal aspiration of blood without respiratory symptoms


display: Neonatal aspiration of blood with respiratory symptoms

names: Neonatal aspiration of blood with pneumonia

names: Neonatal aspiration of blood with pneumonitis


display: Neonatal aspiration of milk and regurgitated food


display: Neonatal aspiration of milk and regurgitated food without respiratory symptoms

names: Neonatal aspiration of milk and regurgitated food NOS


display: Neonatal aspiration of milk and regurgitated food with respiratory symptoms

names: Neonatal aspiration of milk and regurgitated food with pneumonia

names: Neonatal aspiration of milk and regurgitated food with pneumonitis


display: Other neonatal aspiration without respiratory symptoms


display: Other neonatal aspiration with respiratory symptoms

names: Neonatal aspiration with pneumonitis NEC

names: Neonatal aspiration with pneumonitis NOS


display: Interstitial emphysema and related conditions originating in the perinatal period


display: Interstitial emphysema originating in the perinatal period


display: Pneumothorax originating in the perinatal period


display: Pneumomediastinum originating in the perinatal period


display: Pneumopericardium originating in the perinatal period


display: Other conditions related to interstitial emphysema originating in the perinatal period


display: Pulmonary hemorrhage originating in the perinatal period

excludes1: acute idiopathic hemorrhage in infants over 28 days old (R04.81)


display: Tracheobronchial hemorrhage originating in the perinatal period


display: Massive pulmonary hemorrhage originating in the perinatal period


display: Other pulmonary hemorrhages originating in the perinatal period


display: Unspecified pulmonary hemorrhage originating in the perinatal period


display: Chronic respiratory disease originating in the perinatal period

excludes2: respiratory distress of newborn (P22.0-P22.9)


display: Bronchopulmonary dysplasia originating in the perinatal period


display: Other chronic respiratory diseases originating in the perinatal period

names:
Congenital pulmonary fibrosis
Ventilator lung in newborn


display: Unspecified chronic respiratory disease originating in the perinatal period


display: Other respiratory conditions originating in the perinatal period

excludes1: congenital malformations of the respiratory system (Q30-Q34)


display: Primary atelectasis of newborn

names: Primary failure to expand terminal respiratory units

names: Pulmonary hypoplasia associated with short gestation


display: Other and unspecified atelectasis of newborn


display: Resorption atelectasis without respiratory distress syndrome

excludes1: resorption atelectasis with respiratory distress syndrome (P22.0)


display: Other atelectasis of newborn

names:
Partial atelectasis of newborn
Secondary atelectasis of newborn


display: Primary sleep apnea of newborn

names:
Central sleep apnea of newborn
Obstructive sleep apnea of newborn
Sleep apnea of newborn NOS


display: Other apnea of newborn

excludes1: obstructive sleep apnea of newborn (P28.3)

names:
Apnea of prematurity
Obstructive apnea of newborn


display: Respiratory failure of newborn

excludes1: respiratory distress of newborn (P22.0-)


display: Other specified respiratory conditions of newborn


excludes1: early congenital syphilitic rhinitis (A50.05)

names:
Congenital laryngeal stridor
Sniffles in newborn
Snuffles in newborn


display: Respiratory condition of newborn, unspecified


display: Cardiovascular disorders originating in the perinatal period

excludes1: congenital malformations of the circulatory system (Q20-Q28)


display: Pulmonary hypertension of newborn

names: Persistent pulmonary hypertension of newborn


display: Transient myocardial ischemia in newborn


display: Other cardiovascular disorders originating in the perinatal period


display: Cardiovascular disorder originating in the perinatal period, unspecified


display: Congenital viral diseases

names: infections acquired in utero or during birth


display: Congenital herpesviral [herpes simplex] infection


display: Sepsis of newborn due to streptococcus, group B


display: Sepsis of newborn due to other and unspecified streptococci


display: Sepsis of newborn due to unspecified streptococci


display: Sepsis of newborn due to other streptococci


display: Sepsis of newborn due to Staphylococcus aureus


display: Sepsis of newborn due to other and unspecified staphylococci


display: Sepsis of newborn due to unspecified staphylococci


display: Sepsis of newborn due to other staphylococci


display: Sepsis of newborn due to Escherichia coli


display: Bacterial sepsis of newborn, unspecified


display: Other congenital infectious and parasitic diseases

excludes2: necrotizing enterocolitis in newborn (P77.-)

excludes2: ophthalmia neonatorum due to gonococcus (A54.31)


display: Congenital toxoplasmosis

names: Hydrocephalus due to congenital toxoplasmosis


display: Other specified congenital infectious and parasitic diseases


display: Congenital infectious or parasitic disease, unspecified


display: Omphalitis of newborn

excludes1:
omphalitis not of newborn (L08.82)
tetanus omphalitis (A33)
umbilical hemorrhage of newborn (P51.-)


display: Other infections specific to the perinatal period


display: Neonatal infective mastitis

excludes1: noninfective mastitis of newborn (P83.4)


display: Neonatal conjunctivitis and dacryocystitis

names:
Neonatal chlamydial conjunctivitis
Ophthalmia neonatorum NOS


display: Intra-amniotic infection affecting newborn, not elsewhere classified


display: Neonatal skin infection

excludes1: staphylococcal scalded skin syndrome (L00)


display: Other specified infections specific to the perinatal period


display: Infection specific to the perinatal period, unspecified


display: Newborn affected by intrauterine (fetal) blood loss

excludes1: congenital anemia from intrauterine (fetal) blood loss (P61.3)


display: Newborn affected by intrauterine (fetal) blood loss from vasa previa


display: Newborn affected by intrauterine (fetal) blood loss from ruptured cord


display: Newborn affected by intrauterine (fetal) blood loss from placenta


display: Newborn affected by hemorrhage into co-twin


display: Newborn affected by hemorrhage into maternal circulation


display: Newborn affected by intrauterine (fetal) blood loss from cut end of co-twin's cord


display: Newborn affected by other intrauterine (fetal) blood loss


display: Newborn affected by intrauterine (fetal) blood loss, unspecified

names: Newborn affected by fetal hemorrhage NOS


display: Umbilical hemorrhage of newborn

excludes1: umbilical hemorrhage from cut end of co-twins cord (P50.5)


display: Umbilical hemorrhage of newborn, unspecified


display: Intracranial nontraumatic hemorrhage of newborn

excludes1: intracranial hemorrhage due to birth injury (P10.-)

excludes1: intracranial hemorrhage due to other injury (S06.-)

names: intracranial hemorrhage due to anoxia or hypoxia


display: Intraventricular (nontraumatic) hemorrhage, grade 1, of newborn

names: Subependymal hemorrhage (without intraventricular extension)


display: Intraventricular (nontraumatic) hemorrhage, grade 2, of newborn

names: Subependymal hemorrhage with intraventricular extension


display: Intraventricular (nontraumatic) hemorrhage, grade 3 and grade 4, of newborn


display: Intraventricular (nontraumatic) hemorrhage, grade 3, of newborn

names: Subependymal hemorrhage with intraventricular extension with enlargement of ventricle


display: Intraventricular (nontraumatic) hemorrhage, grade 4, of newborn

names: Subependymal hemorrhage with intracerebral extension


display: Unspecified intraventricular (nontraumatic) hemorrhage of newborn


display: Intracerebral (nontraumatic) hemorrhage of newborn


display: Subarachnoid (nontraumatic) hemorrhage of newborn


display: Cerebellar (nontraumatic) and posterior fossa hemorrhage of newborn


display: Other intracranial (nontraumatic) hemorrhages of newborn


display: Intracranial (nontraumatic) hemorrhage of newborn, unspecified


display: Other neonatal hemorrhages

excludes1: newborn affected by (intrauterine) blood loss (P50.-)

excludes1: pulmonary hemorrhage originating in the perinatal period (P26.-)


display: Neonatal hematemesis

excludes1: neonatal hematemesis due to swallowed maternal blood (P78.2)


display: Neonatal melena

excludes1: neonatal melena due to swallowed maternal blood (P78.2)


display: Other neonatal gastrointestinal hemorrhage


display: Neonatal cutaneous hemorrhage

excludes2: bruising of scalp due to birth injury (P12.3)

excludes2: cephalhematoma due to birth injury (P12.0)

names:
Neonatal bruising
Neonatal ecchymoses
Neonatal petechiae
Neonatal superficial hematomata


display: Hemolytic disease of newborn, unspecified


display: Hydrops fetalis due to hemolytic disease


display: Hydrops fetalis due to other and unspecified hemolytic disease


display: Hydrops fetalis due to unspecified hemolytic disease


display: Hydrops fetalis due to other hemolytic disease


display: Neonatal jaundice due to other excessive hemolysis

excludes1: jaundice due to isoimmunization (P55-P57)


display: Neonatal jaundice due to drugs or toxins transmitted from mother or given to newborn


display: Neonatal jaundice due to drugs or toxins transmitted from mother


display: Neonatal jaundice due to drugs or toxins given to newborn


display: Neonatal jaundice due to swallowed maternal blood


display: Neonatal jaundice due to other specified excessive hemolysis


display: Neonatal jaundice due to excessive hemolysis, unspecified


display: Neonatal jaundice from other and unspecified causes

excludes1: jaundice due to inborn errors of metabolism (E70-E88)


display: Neonatal jaundice associated with preterm delivery

names: Jaundice due to delayed conjugation associated with preterm delivery


display: Neonatal jaundice from other and unspecified hepatocellular damage


display: Neonatal jaundice from unspecified hepatocellular damage


display: Neonatal jaundice from other hepatocellular damage

names:
Neonatal giant cell hepatitis
Neonatal (idiopathic) hepatitis


display: Neonatal jaundice from breast milk inhibitor


display: Neonatal jaundice from other specified causes


display: Neonatal jaundice, unspecified

names: Neonatal physiological jaundice (intense)(prolonged) NOS


display: Disseminated intravascular coagulation of newborn


display: Other perinatal hematological disorders

excludes1: transient hypogammaglobulinemia of infancy (D80.7)


display: Transient neonatal thrombocytopenia

names: Neonatal thrombocytopenia due to exchange transfusion

names: Neonatal thrombocytopenia due to idiopathic maternal thrombocytopenia

names: Neonatal thrombocytopenia due to isoimmunization


display: Other congenital anemias, not elsewhere classified


display: Transient neonatal neutropenia

excludes1: congenital neutropenia (nontransient) (D70.0)


display: Other transient neonatal disorders of coagulation


display: Other specified perinatal hematological disorders


display: Perinatal hematological disorder, unspecified


display: Transitory disorders of carbohydrate metabolism specific to newborn


display: Syndrome of infant of mother with gestational diabetes

excludes1: newborn (with hypoglycemia) affected by maternal (pre-existing) diabetes mellitus (P70.1)

excludes1: syndrome of infant of a diabetic mother (P70.1)

names: Newborn (with hypoglycemia) affected by maternal gestational diabetes


display: Syndrome of infant of a diabetic mother

excludes1: newborn (with hypoglycemia) affected by maternal gestational diabetes (P70.0)

excludes1: syndrome of infant of mother with gestational diabetes (P70.0)

names: Newborn (with hypoglycemia) affected by maternal (pre-existing) diabetes mellitus


display: Other transitory disorders of carbohydrate metabolism of newborn


display: Transitory disorder of carbohydrate metabolism of newborn, unspecified


display: Transitory neonatal disorders of calcium and magnesium metabolism


display: Neonatal tetany without calcium or magnesium deficiency


display: Other transitory neonatal disorders of calcium and magnesium metabolism


display: Transitory neonatal disorder of calcium and magnesium metabolism, unspecified


display: Other transitory neonatal endocrine disorders

excludes1: congenital hypothyroidism with or without goiter (E03.0-E03.1)


display: Neonatal goiter, not elsewhere classified

names: Transitory congenital goiter with normal functioning


display: Other transitory neonatal disorders of thyroid function, not elsewhere classified


display: Other specified transitory neonatal endocrine disorders


display: Transitory neonatal endocrine disorder, unspecified


display: Other transitory neonatal electrolyte and metabolic disturbances


display: Late metabolic acidosis of newborn

excludes1: (fetal) metabolic acidosis of newborn (P19)


display: Disturbances of sodium balance of newborn


display: Disturbances of potassium balance of newborn


display: Other transitory electrolyte disturbances of newborn


display: Disturbances of chlorine balance of newborn


display: Hyperchloremia of newborn

excludes2: late metabolic acidosis of the newborn (P77.0)


display: Other transitory electrolyte disturbance of newborn


display: Other transitory metabolic disturbances of newborn

names: Amino-acid metabolic disorders described as transitory


display: Transitory metabolic disturbance of newborn, unspecified


display: Meconium plug syndrome

excludes1: meconium ileus in cystic fibrosis (E84.11)


display: Intestinal obstruction due to inspissated milk


display: Other specified intestinal obstruction of newborn

excludes1: intestinal obstruction classifiable to K56.-


display: Intestinal obstruction of newborn, unspecified


display: Stage 1 necrotizing enterocolitis in newborn

names: Necrotizing enterocolitis without pneumatosis, without perforation


display: Stage 2 necrotizing enterocolitis in newborn

names: Necrotizing enterocolitis with pneumatosis, without perforation


display: Stage 3 necrotizing enterocolitis in newborn

names: Necrotizing enterocolitis with perforation

names: Necrotizing enterocolitis with pneumatosis and perforation


display: Necrotizing enterocolitis in newborn, unspecified

names: Necrotizing enterocolitis in newborn, NOS


display: Other perinatal digestive system disorders

excludes1: neonatal gastrointestinal hemorrhages (P54.0-P54.3)


display: Neonatal hematemesis and melena due to swallowed maternal blood


display: Other specified perinatal digestive system disorders


display: Gestational alloimmune liver disease

names:
GALD
Neonatal hemochromatosis


display: Perinatal digestive system disorder, unspecified


display: Cold injury syndrome

names: Severe and usually chronic hypothermia associated with a pink flushed appearance, edema and neurological and biochemical abnormalities.


display: Other disturbances of temperature regulation of newborn


display: Other specified disturbances of temperature regulation of newborn


display: Disturbance of temperature regulation of newborn, unspecified


display: Other conditions of integument specific to newborn

excludes1: congenital malformations of skin and integument (Q80-Q84)

excludes1: hydrops fetalis due to hemolytic disease (P56.-)

excludes1: staphylococcal scalded skin syndrome (L00)

excludes2:
cradle cap (L21.0)
diaper [napkin] dermatitis (L22)


display: Hydrops fetalis not due to hemolytic disease


display: Other and unspecified edema specific to newborn


display: Other specified conditions of integument specific to newborn


display: Umbilical granuloma

excludes2: Granulomatous disorder of the skin and subcutaneous tissue, unspecified (L92.9)


names:
Bronze baby syndrome
Neonatal scleroderma
Urticaria neonatorum


display: Condition of the integument specific to newborn, unspecified


display: Other problems with newborn

excludes1: intracranial hemorrhage due to anoxia or hypoxia (P52.-)

excludes1: hypoxic ischemic encephalopathy [HIE] (P91.6-)

excludes1: late metabolic acidosis of newborn (P74.0)

names: Mixed metabolic and respiratory acidosis of newborn


display: Convulsions of newborn

excludes1: benign myoclonic epilepsy in infancy (G40.3-)

excludes1: benign neonatal convulsions (familial) (G40.3-)


display: Other disturbances of cerebral status of newborn


display: Acquired periventricular cysts of newborn


display: Hypoxic ischemic encephalopathy [HIE]

excludes1:
Neonatal cerebral depression (P91.4)
Neonatal cerebral irritability (P91.3)
Neonatal coma (P91.5)


display: Hypoxic ischemic encephalopathy [HIE], unspecified


display: Mild hypoxic ischemic encephalopathy [HIE]


display: Moderate hypoxic ischemic encephalopathy [HIE]


display: Severe hypoxic ischemic encephalopathy [HIE]


display: Other specified disturbances of cerebral status of newborn


display: Neonatal encephalopathy in diseases classified elsewhere


display: Disturbance of cerebral status of newborn, unspecified


display: Feeding problems of newborn

excludes1: feeding problems in child over 28 days old (R63.3)


display: Vomiting of newborn

excludes1: vomiting of child over 28 days old (R11.-)


display: Bilious vomiting of newborn

excludes1: bilious vomiting in child over 28 days old (R11.14)


display: Other vomiting of newborn

excludes1: regurgitation of food in newborn (P92.1)


display: Neonatal difficulty in feeding at breast


display: Failure to thrive in newborn

excludes1: failure to thrive in child over 28 days old (R62.51)


display: Reactions and intoxications due to drugs administered to newborn

excludes1: jaundice due to drugs or toxins transmitted from mother or given to newborn (P58.4-)

excludes1: reactions and intoxications from maternal opiates, tranquilizers and other medication (P04.0-P04.1, P04.4-)

excludes1: withdrawal symptoms from maternal use of drugs of addiction (P96.1)

excludes1: withdrawal symptoms from therapeutic use of drugs in newborn (P96.2)

names: reactions and intoxications due to drugs administered to fetus affecting newborn


display: Grey baby syndrome

names: Grey syndrome from chloramphenicol administration in newborn


display: Other reactions and intoxications due to drugs administered to newborn


display: Other disorders of muscle tone of newborn


display: Disorder of muscle tone of newborn, unspecified


display: Stillbirth

excludes1: maternal care for intrauterine death (O36.4)

excludes1: outcome of delivery, stillbirth (Z37.1, Z37.3, Z37.4, Z37.7)

names:
Deadborn fetus NOS
Fetal death of unspecified cause
Stillbirth NOS


display: Other conditions originating in the perinatal period


display: Neonatal withdrawal symptoms from maternal use of drugs of addiction

excludes1: reactions and intoxications from maternal opiates and tranquilizers administered during labor and delivery (P04.0)

names: Drug withdrawal syndrome in infant of dependent mother


display: Withdrawal symptoms from therapeutic use of drugs in newborn


display: Complication to newborn due to (fetal) intrauterine procedure

excludes2: newborn affected by amniocentesis (P00.6)


display: Other specified conditions originating in the perinatal period


display: Exposure to (parental) (environmental) tobacco smoke in the perinatal period

excludes2: newborn affected by in utero exposure to tobacco (P04.2)

excludes2: exposure to environmental tobacco smoke after the perinatal period (Z77.22)


display: Meconium staining

excludes1: meconium passage during delivery (P03.82)


display: Condition originating in the perinatal period, unspecified


display: Anencephaly

names: Acephaly Acrania Amyelencephaly Hemianencephaly Hemicephaly


display: Encephalocele

names:
Arnold-Chiari syndrome, type III
encephalocystocele
encephalomyelocele
hydroencephalocele
hydromeningocele, cranial
meningocele, cerebral
meningoencephalocele


display: Microcephaly

names: hydromicrocephaly micrencephalon


display: Congenital hydrocephalus

excludes1: Arnold-Chiari syndrome, type II (Q07.0-)

excludes1: hydrocephalus due to congenital toxoplasmosis (P37.1)

excludes1: hydrocephalus with spina bifida (Q05.0-Q05.4)


display: Malformations of aqueduct of Sylvius

names: Obstruction of aqueduct of Sylvius, congenital


display: Atresia of foramina of Magendie and Luschka


display: Other congenital malformations of brain

excludes1:
cyclopia (Q87.0)
macrocephaly (Q75.3)


display: Congenital malformations of corpus callosum


display: Other reduction deformities of brain

excludes1: congenital malformations of corpus callosum (Q04.0)

names:
Absence of part of brain
Agenesis of part of brain
Agyria
Aplasia of part of brain
Hydranencephaly
Hypoplasia of part of brain
Lissencephaly
Microgyria
Pachygyria


display: Congenital cerebral cysts

names: Porencephaly Schizencephaly


display: Other specified congenital malformations of brain

names:
Arnold-Chiari syndrome, type IV
Macrogyria


display: Congenital malformation of brain, unspecified

names: Congenital disease or lesion NOS of brain

names: Multiple anomalies NOS of brain, congenital


display: Spina bifida

names:
hydromeningocele (spinal)
meningocele (spinal)
meningomyelocele
myelocele
myelomeningocele
rachischisis
spina bifida (aperta)(cystica)
syringomyelocele


display: Cervical spina bifida with hydrocephalus


display: Thoracic spina bifida with hydrocephalus

names: Thoracolumbar spina bifida with hydrocephalus


display: Lumbar spina bifida with hydrocephalus

names: Lumbosacral spina bifida with hydrocephalus


display: Unspecified spina bifida with hydrocephalus


display: Cervical spina bifida without hydrocephalus


display: Thoracic spina bifida without hydrocephalus

names:
Dorsal spina bifida NOS
Thoracolumbar spina bifida NOS


display: Lumbar spina bifida without hydrocephalus


display: Sacral spina bifida without hydrocephalus


display: Other congenital malformations of spinal cord


display: Hypoplasia and dysplasia of spinal cord

names:
Atelomyelia
Myelatelia
Myelodysplasia of spinal cord


display: Other congenital cauda equina malformations


display: Other specified congenital malformations of spinal cord


display: Congenital malformation of spinal cord, unspecified

names: Congenital disease or lesion NOS of spinal cord


display: Other congenital malformations of nervous system

excludes2: congenital central alveolar hypoventilation syndrome (G47.35)

excludes2: familial dysautonomia [Riley-Day] (G90.1)


display: Arnold-Chiari syndrome

excludes1: Arnold-Chiari syndrome, type III (Q01.-)


display: Arnold-Chiari syndrome without spina bifida or hydrocephalus


display: Arnold-Chiari syndrome with spina bifida


display: Arnold-Chiari syndrome with hydrocephalus


display: Arnold-Chiari syndrome with spina bifida and hydrocephalus


display: Other specified congenital malformations of nervous system

names:
Agenesis of nerve
Displacement of brachial plexus
Jaw-winking syndrome
Marcus Gunn's syndrome


display: Congenital malformation of nervous system, unspecified

names: Congenital anomaly NOS of nervous system

names: Congenital deformity NOS of nervous system

names: Congenital disease or lesion NOS of nervous system


display: Congenital malformations of eyelid, lacrimal apparatus and orbit

excludes1:
cryptophthalmos NOS (Q11.2)
cryptophthalmos syndrome (Q87.0)


display: Other congenital malformations of eyelid

names: Congenital absence or agenesis of eyelid


display: Absence and agenesis of lacrimal apparatus


display: Congenital stenosis and stricture of lacrimal duct


display: Other congenital malformations of lacrimal apparatus

names: Congenital malformation of lacrimal apparatus NOS


display: Anophthalmos, microphthalmos and macrophthalmos


display: Other anophthalmos

names:
Anophthalmos NOS
Agenesis of eye
Aplasia of eye


display: Microphthalmos

names:
Cryptophthalmos NOS
Dysplasia of eye
Hypoplasia of eye
Rudimentary eye


display: Macrophthalmos

excludes1: macrophthalmos in congenital glaucoma (Q15.0)


display: Congenital lens malformation, unspecified


display: Congenital malformations of anterior segment of eye


display: Other congenital malformations of iris

names:
Anisocoria, congenital
Atresia of pupil
Congenital malformation of iris NOS
Corectopia


display: Other congenital corneal malformations

names:
Congenital malformation of cornea NOS
Microcornea
Peter's anomaly


display: Other congenital malformations of anterior segment of eye


display: Congenital malformation of anterior segment of eye, unspecified


display: Congenital malformations of posterior segment of eye


display: Congenital malformation of vitreous humor


display: Other congenital malformations of posterior segment of eye


display: Congenital malformation of posterior segment of eye, unspecified


display: Other congenital malformations of eye

excludes1:
congenital nystagmus (H55.01)
ocular albinism (E70.31-)
optic nerve hypoplasia (H47.03-)
retinitis pigmentosa (H35.52)


display: Congenital glaucoma

names:
Axenfeld's anomaly
Buphthalmos
Glaucoma of childhood
Glaucoma of newborn
Hydrophthalmos
Keratoglobus, congenital, with glaucoma
Macrocornea with glaucoma
Macrophthalmos in congenital glaucoma
Megalocornea with glaucoma


display: Other specified congenital malformations of eye


display: Congenital malformation of eye, unspecified

names:
Congenital anomaly of eye
Congenital deformity of eye


display: Congenital malformations of ear causing impairment of hearing


display: Congenital absence, atresia and stricture of auditory canal (external)

names: Congenital atresia or stricture of osseous meatus


display: Other congenital malformations of middle ear

names: Congenital malformation of middle ear NOS


display: Congenital malformation of inner ear

names: Congenital anomaly of membranous labyrinth


display: Congenital malformation of ear causing impairment of hearing, unspecified


display: Other congenital malformations of ear

excludes1: congenital malformations of ear with impairment of hearing (Q16.0-Q16.9)


display: Accessory auricle

names:
Accessory tragus
Polyotia
Preauricular appendage or tag
Supernumerary ear
Supernumerary lobule


display: Other specified congenital malformations of ear


display: Congenital malformation of ear, unspecified


display: Other congenital malformations of face and neck

excludes1: congenital malformations of skull and face bones (Q75.-)

excludes1: dentofacial anomalies [including malocclusion] (M26.-)

excludes1: malformation syndromes affecting facial appearance (Q87.0)


display: Sinus, fistula and cyst of branchial cleft


display: Preauricular sinus and cyst

names:
Fistula of auricle, congenital
Cervicoaural fistula


display: Other branchial cleft malformations

names:
Branchial cleft malformation NOS
Cervical auricle
Otocephaly


display: Other specified congenital malformations of face and neck

names:
Medial cyst of face and neck
Medial fistula of face and neck
Medial sinus of face and neck


display: Congenital malformation of face and neck, unspecified


display: Congenital malformations of cardiac chambers and connections

excludes1: dextrocardia with situs inversus (Q89.3)

excludes1: mirror-image atrial arrangement with situs inversus (Q89.3)


names: Transposition of great vessels (complete)


display: Double inlet ventricle

names:
Common ventricle
Cor triloculare biatriatum
Single ventricle


display: Discordant atrioventricular connection

names:
Corrected transposition
Levotransposition
Ventricular inversion


display: Isomerism of atrial appendages

names: Isomerism of atrial appendages with asplenia or polysplenia


display: Other congenital malformations of cardiac chambers and connections


display: Congenital malformation of cardiac chambers and connections, unspecified


display: Congenital malformations of cardiac septa


display: Atrial septal defect

names: Patent or persistent ostium secundum defect (type II)

names: Patent or persistent sinus venosus defect


display: Atrioventricular septal defect

names: Ostium primum atrial septal defect (type I)


display: Tetralogy of Fallot

names: Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.


display: Aortopulmonary septal defect

names:
Aortic septal defect
Aortopulmonary window


display: Other congenital malformations of cardiac septa

names:
Eisenmenger's defect
Pentalogy of Fallot


display: Congenital malformation of cardiac septum, unspecified


display: Congenital malformations of pulmonary and tricuspid valves


display: Congenital pulmonary valve insufficiency

names: Congenital pulmonary valve regurgitation


display: Other congenital malformations of pulmonary valve

names: Congenital malformation of pulmonary valve NOS


display: Other congenital malformations of tricuspid valve


display: Congenital malformation of tricuspid valve, unspecified


display: Congenital malformations of aortic and mitral valves


display: Congenital stenosis of aortic valve

excludes1: congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)

excludes1: supravalvular aortic stenosis (congenital) (Q25.3)

names:
Congenital aortic atresia
Congenital aortic stenosis NOS


display: Congenital insufficiency of aortic valve

names:
Bicuspid aortic valve
Congenital aortic insufficiency


display: Other congenital malformations of aortic and mitral valves


display: Congenital malformation of aortic and mitral valves, unspecified


display: Dextrocardia

excludes1: isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)


display: Other specified congenital malformations of heart

names: Congenital diverticulum of left ventricle


display: Congenital malformation of heart, unspecified

names:
Congenital anomaly of heart
Congenital disease of heart


display: Congenital malformations of great arteries


display: Patent ductus arteriosus

names:
Patent ductus Botallo
Persistent ductus arteriosus


display: Coarctation of aorta

names: Coarctation of aorta (preductal) (postductal)


display: Supravalvular aortic stenosis

excludes1: congenital stenosis of aortic valve (Q23.0)


display: Other congenital malformations of aorta

excludes1: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)


display: Congenital malformation of aorta unspecified


display: Congenital aneurysm of aorta

names:
Congenital aneurysm of aortic root
Congenital aneurysm of aortic sinus


names:
Aortic arch
Bovine arch


display: Other congenital malformations of pulmonary artery


display: Congenital pulmonary arteriovenous malformation

names: Congenital pulmonary arteriovenous aneurysm


names:
Aberrant pulmonary artery
Agenesis of pulmonary artery
Congenital aneurysm of pulmonary artery
Congenital anomaly of pulmonary artery
Hypoplasia of pulmonary artery


display: Other congenital malformations of other great arteries


display: Congenital malformation of great arteries, unspecified


display: Congenital stenosis of vena cava

names: Congenital stenosis of vena cava (inferior)(superior)


display: Total anomalous pulmonary venous connection

names: Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic

names: Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic


display: Partial anomalous pulmonary venous connection

names: Partial anomalous pulmonary venous return


display: Anomalous pulmonary venous connection, unspecified


display: Other congenital malformations of great veins

names: Absence of vena cava (inferior) (superior)

names: Azygos continuation of inferior vena cava


display: Congenital malformation of great vein, unspecified

names: Congenital anomaly of vena cava (inferior) (superior) NOS


display: Other congenital malformations of peripheral vascular system

excludes2: anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)

excludes2: anomalies of pulmonary artery (Q25.5-Q25.7)


display: Congenital absence and hypoplasia of umbilical artery


display: Other congenital malformations of renal artery

names: Congenital malformation of renal artery NOS


display: Arteriovenous malformation (peripheral)

excludes2: arteriovenous malformation of cerebral vessels (Q28.2)

excludes2: arteriovenous malformation of precerebral vessels (Q28.0)


display: Arteriovenous malformation, site unspecified


display: Arteriovenous malformation of vessel of upper limb


display: Arteriovenous malformation of vessel of lower limb


display: Arteriovenous malformation of digestive system vessel


display: Arteriovenous malformation of renal vessel


display: Other specified congenital malformations of peripheral vascular system

names:
Absence of peripheral vascular system
Atresia of peripheral vascular system
Congenital aneurysm (peripheral)
Congenital stricture, artery
Congenital varix


display: Congenital malformation of peripheral vascular system, unspecified


display: Other congenital malformations of circulatory system

excludes1: ruptured cerebral arteriovenous malformation (I60.8)

excludes1: ruptured malformation of precerebral vessels (I72.0)

excludes2:
congenital peripheral aneurysm (Q27.8)
congenital pulmonary aneurysm (Q25.79)
congenital retinal aneurysm (Q14.1)


display: Arteriovenous malformation of precerebral vessels

names: Congenital arteriovenous precerebral aneurysm (nonruptured)


display: Other malformations of precerebral vessels

names: Congenital malformation of precerebral vessels NOS

names: Congenital precerebral aneurysm (nonruptured)


display: Arteriovenous malformation of cerebral vessels

names: Congenital arteriovenous cerebral aneurysm (nonruptured)


display: Other malformations of cerebral vessels

names: Congenital cerebral aneurysm (nonruptured)

names: Congenital malformation of cerebral vessels NOS


display: Other specified congenital malformations of circulatory system

names:
Congenital aneurysm, specified site NEC
Spinal vessel anomaly


display: Congenital malformation of circulatory system, unspecified


display: Congenital malformations of nose

excludes1: congenital deviation of nasal septum (Q67.4)


display: Choanal atresia

names: Congenital stenosis of nares (anterior) (posterior)


display: Other congenital malformations of nose

names:
Accessory nose
Congenital anomaly of nasal sinus wall


display: Congenital malformation of nose, unspecified


display: Congenital malformations of larynx

excludes1: congenital laryngeal stridor NOS (P28.89)


display: Web of larynx

names:
Glottic web of larynx
Subglottic web of larynx
Web of larynx NOS


display: Other congenital malformations of larynx

names:
Absence of larynx
Agenesis of larynx
Atresia of larynx
Congenital cleft thyroid cartilage
Congenital fissure of epiglottis
Congenital stenosis of larynx NEC
Posterior cleft of cricoid cartilage


display: Congenital malformation of larynx, unspecified


display: Congenital malformations of trachea and bronchus


display: Other congenital malformations of trachea

names: Congenital anomaly of tracheal cartilage


display: Other congenital malformations of bronchus

names:
Absence of bronchus
Agenesis of bronchus
Atresia of bronchus
Congenital diverticulum of bronchus
Congenital malformation of bronchus NOS


display: Congenital cystic lung

excludes1: cystic lung disease, acquired or unspecified (J98.4)

names:
Congenital cystic lung disease
Congenital honeycomb lung
Congenital polycystic lung disease


display: Congenital hypoplasia and dysplasia of lung

excludes1: pulmonary hypoplasia associated with short gestation (P28.0)


display: Congenital malformation of lung, unspecified


display: Other congenital malformations of respiratory system


display: Other specified congenital malformations of respiratory system


display: Congenital malformation of respiratory system, unspecified

names: Congenital absence of respiratory system

names: Congenital anomaly of respiratory system NOS


display: Cleft palate

names:
fissure of palate
palatoschisis


display: Cleft hard palate with cleft soft palate


display: Cleft lip

names:
cheiloschisis
congenital fissure of lip
harelip
labium leporinum


display: Cleft hard palate with bilateral cleft lip


display: Cleft hard palate with unilateral cleft lip


display: Cleft soft palate with bilateral cleft lip


display: Cleft soft palate with unilateral cleft lip


display: Cleft hard and soft palate with bilateral cleft lip


display: Cleft hard and soft palate with unilateral cleft lip

names: Cleft hard and soft palate with cleft lip NOS


display: Unspecified cleft palate with bilateral cleft lip


display: Unspecified cleft palate with unilateral cleft lip


display: Other congenital malformations of tongue, mouth and pharynx

excludes1:
dentofacial anomalies (M26.-)
macrostomia (Q18.4)
microstomia (Q18.5)


display: Congenital malformations of lips, not elsewhere classified

excludes1:
cleft lip (Q36.-)
cleft lip with cleft palate (Q37.-)
macrocheilia (Q18.6)
microcheilia (Q18.7)

names:
Congenital fistula of lip
Congenital malformation of lip NOS
Van der Woude's syndrome


display: Other congenital malformations of tongue

names:
Aglossia
Bifid tongue
Congenital adhesion of tongue
Congenital fissure of tongue
Congenital malformation of tongue NOS
Double tongue
Hypoglossia
Hypoplasia of tongue
Microglossia


display: Congenital malformations of salivary glands and ducts

names: Congenital absence of salivary glands and ducts

names: Congenital accessory salivary glands and ducts


display: Congenital malformations of palate, not elsewhere classified

excludes1:
cleft palate (Q35.-)
cleft palate with cleft lip (Q37.-)

names:
Congenital absence of uvula
Congenital malformation of palate NOS
Congenital high arched palate


display: Other congenital malformations of pharynx

names:
Congenital malformation of pharynx NOS
Imperforate pharynx


display: Atresia of esophagus with tracheo-esophageal fistula

names: Atresia of esophagus with broncho-esophageal fistula


display: Congenital tracheo-esophageal fistula without atresia

names: Congenital tracheo-esophageal fistula NOS


display: Congenital stenosis and stricture of esophagus


display: Other congenital malformations of esophagus

names:
Congenital absence of esophagus
Congenital displacement of esophagus
Congenital duplication of esophagus


display: Congenital malformation of esophagus, unspecified


display: Other congenital malformations of upper alimentary tract


display: Congenital hypertrophic pyloric stenosis

names:
Congenital or infantile constriction
Congenital or infantile hypertrophy
Congenital or infantile spasm
Congenital or infantile stenosis
Congenital or infantile stricture


display: Congenital hiatus hernia

names: Congenital displacement of cardia through esophageal hiatus


display: Other specified congenital malformations of stomach

names:
Congenital displacement of stomach
Congenital diverticulum of stomach
Congenital hourglass stomach
Congenital duplication of stomach
Megalogastria
Microgastria


display: Congenital malformation of stomach, unspecified


display: Other specified congenital malformations of upper alimentary tract


display: Congenital malformation of upper alimentary tract, unspecified

names: Congenital anomaly of upper alimentary tract

names: Congenital deformity of upper alimentary tract


display: Congenital absence, atresia and stenosis of small intestine

excludes1: cystic fibrosis with intestinal manifestation (E84.11)

excludes1: meconium ileus NOS (without cystic fibrosis) (P76.0)

names: congenital obstruction, occlusion or stricture of small intestine or intestine NOS


display: Congenital absence, atresia and stenosis of duodenum


display: Congenital absence, atresia and stenosis of jejunum

names:
Apple peel syndrome
Imperforate jejunum


display: Congenital absence, atresia and stenosis of ileum


display: Congenital absence, atresia and stenosis of other specified parts of small intestine


display: Congenital absence, atresia and stenosis of small intestine, part unspecified

names: Congenital absence, atresia and stenosis of intestine NOS


display: Congenital absence, atresia and stenosis of large intestine

names: congenital obstruction, occlusion and stricture of large intestine


display: Congenital absence, atresia and stenosis of rectum with fistula


display: Congenital absence, atresia and stenosis of rectum without fistula


display: Congenital absence, atresia and stenosis of anus with fistula


display: Congenital absence, atresia and stenosis of anus without fistula


display: Congenital absence, atresia and stenosis of other parts of large intestine


display: Congenital absence, atresia and stenosis of large intestine, part unspecified


display: Other congenital malformations of intestine


display: Meckel's diverticulum (displaced) (hypertrophic)

names:
Persistent omphalomesenteric duct
Persistent vitelline duct


display: Hirschsprung's disease

names:
Aganglionosis
Congenital (aganglionic) megacolon


display: Other congenital functional disorders of colon


display: Congenital malformations of intestinal fixation

names: Congenital omental, anomalous adhesions [bands]

names: Insufficient rotation of cecum and colon


display: Congenital fistula of rectum and anus

excludes1: congenital fistula of anus with absence, atresia and stenosis (Q42.2)

excludes1: congenital fistula of rectum with absence, atresia and stenosis (Q42.0)

excludes1: congenital urethrorectal fistula (Q64.73)


display: Other specified congenital malformations of intestine

names:
Congenital blind loop syndrome
Congenital diverticulitis, colon
Congenital diverticulum, intestine
Dolichocolon
Megaloappendix
Megaloduodenum
Microcolon
Transposition of appendix
Transposition of colon
Transposition of intestine


display: Congenital malformation of intestine, unspecified


display: Congenital malformations of gallbladder, bile ducts and liver


display: Agenesis, aplasia and hypoplasia of gallbladder


display: Other congenital malformations of gallbladder

names: Congenital malformation of gallbladder NOS


display: Congenital stenosis and stricture of bile ducts


display: Other congenital malformations of bile ducts

names: Congenital malformation of bile duct NOS


display: Other congenital malformations of liver

names:
Accessory liver
Alagille's syndrome
Congenital absence of liver
Congenital hepatomegaly
Congenital malformation of liver NOS


display: Other congenital malformations of digestive system

excludes2:
congenital diaphragmatic hernia (Q79.0)
congenital hiatus hernia (Q40.1)


display: Agenesis, aplasia and hypoplasia of pancreas


display: Other congenital malformations of pancreas and pancreatic duct

excludes1:
congenital diabetes mellitus (E10.-)
cystic fibrosis (E84.0-E84.9)
fibrocystic disease of pancreas (E84.-)
neonatal diabetes mellitus (P70.2)

names: Congenital malformation of pancreas or pancreatic duct NOS


display: Other specified congenital malformations of digestive system

names: Absence (complete) (partial) of alimentary tract NOS

names: Malposition, congenital of digestive system


display: Congenital malformation of digestive system, unspecified

names: Congenital deformity of digestive system


display: Congenital malformations of ovaries, fallopian tubes and broad ligaments


display: Embryonic cyst of broad ligament

names:
Epoophoron cyst
Parovarian cyst


display: Other congenital malformations of fallopian tube and broad ligament

names: Absence of fallopian tube and broad ligament

names: Accessory fallopian tube and broad ligament

names: Atresia of fallopian tube and broad ligament

names: Congenital malformation of fallopian tube or broad ligament NOS


display: Congenital malformations of uterus and cervix


display: Doubling of uterus with doubling of cervix and vagina


display: Doubling of uterus with doubling of cervix and vagina without obstruction

names: Doubling of uterus with doubling of cervix and vagina NOS


display: Doubling of uterus with doubling of cervix and vagina with obstruction


display: Other doubling of uterus

names:
Doubling of uterus NOS
Septate uterus


display: Other doubling of uterus, other specified


display: Unicornate uterus

names: Unicornate uterus with or without a separate uterine horn


display: Congenital fistulae between uterus and digestive and urinary tracts


display: Other congenital malformations of uterus and cervix


display: Other congenital malformations of uterus


display: Other congenital malformations of cervix


display: Congenital malformation of uterus and cervix, unspecified


display: Other congenital malformations of female genitalia


display: Doubling of vagina

excludes1: doubling of vagina with doubling of uterus and cervix (Q51.1-)


display: Longitudinal vaginal septum, nonobstructing


display: Longitudinal vaginal septum, obstructing, right side


display: Longitudinal vaginal septum, obstructing, left side


display: Longitudinal vaginal septum, microperforate, right side


display: Longitudinal vaginal septum, microperforate, left side


display: Other and unspecified longitudinal vaginal septum


display: Other congenital malformations of vagina

names:
Canal of Nuck cyst, congenital
Congenital malformation of vagina NOS
Embryonic vaginal cyst
Gartner's duct cyst


display: Other and unspecified congenital malformations of vulva


display: Unspecified congenital malformations of vulva


display: Other specified congenital malformations of female genitalia


display: Congenital malformation of female genitalia, unspecified


display: Unspecified undescended testicle, unilateral


display: Undescended testicle, unspecified, bilateral


display: Hypospadias, balanic

names:
Hypospadias, coronal
Hypospadias, glandular


display: Other congenital malformations of male genital organs

excludes1:
congenital hydrocele (P83.5)
hypospadias (Q54.-)


display: Other and unspecified congenital malformations of testis and scrotum


display: Unspecified congenital malformations of testis and scrotum

names: Congenital malformation of testis or scrotum NOS


display: Other congenital malformations of testis and scrotum


display: Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

names: Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS


display: Hidden penis

names:
Buried penis
Concealed penis


display: Other specified congenital malformations of male genital organs


display: Congenital malformation of male genital organ, unspecified

names: Congenital anomaly of male genital organ

names: Congenital deformity of male genital organ


display: Indeterminate sex and pseudohermaphroditism

excludes1: androgen insensitivity syndrome (E34.5-)

excludes1: chimera 46,XX/46,XY true hermaphrodite (Q99.0)

excludes1: female pseudohermaphroditism with adrenocortical disorder (E25.-)

excludes1: pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)


display: Hermaphroditism, not elsewhere classified


display: Male pseudohermaphroditism, not elsewhere classified

names:
46, XY with streak gonads
Male pseudohermaphroditism NOS


display: Female pseudohermaphroditism, not elsewhere classified


display: Renal agenesis and other reduction defects of kidney

names:
congenital absence of kidney
congenital atrophy of kidney
infantile atrophy of kidney


display: Cystic kidney disease

excludes1:
acquired cyst of kidney (N28.1)
Potter's syndrome (Q60.6)


display: Renal dysplasia

excludes1: polycystic kidney disease (Q61.11-Q61.3)

names:
Multicystic dysplastic kidney
Multicystic kidney (development)
Multicystic kidney disease
Multicystic renal dysplasia


display: Medullary cystic kidney

names:
Nephronopthisis
Sponge kidney NOS


display: Other cystic kidney diseases

names: Fibrocystic renal degeneration or disease


display: Congenital obstructive defects of renal pelvis and congenital malformations of ureter


display: Congenital occlusion of ureter, unspecified


display: Congenital occlusion of ureteropelvic junction


display: Congenital occlusion of ureterovesical orifice


display: Other obstructive defects of renal pelvis and ureter


display: Duplication of ureter

names:
Accessory ureter
Double ureter


display: Anomalous implantation of ureter

names:
Ectopia of ureter
Ectopic ureter


display: Other congenital malformations of ureter


display: Other congenital malformations of kidney


display: Ectopic kidney

names:
Congenital displaced kidney
Malrotation of kidney


display: Other specified congenital malformations of kidney


display: Congenital malformation of kidney, unspecified


display: Other congenital malformations of urinary system


display: Exstrophy of urinary bladder, unspecified


display: Other atresia and stenosis of urethra and bladder neck


display: Congenital bladder neck obstruction

names: Congenital obstruction of vesicourethral orifice


names: Atresia and stenosis of urethra and bladder neck NOS


display: Malformation of urachus

names:
Cyst of urachus
Patent urachus
Prolapse of urachus


display: Congenital absence of bladder and urethra


display: Other and unspecified congenital malformations of bladder and urethra

excludes1: congenital prolapse of bladder (mucosa) (Q79.4)


display: Unspecified congenital malformation of bladder and urethra


display: Other congenital malformations of bladder and urethra


display: Other specified congenital malformations of urinary system


display: Congenital malformation of urinary system, unspecified

names: Congenital anomaly NOS of urinary system

names: Congenital deformity NOS of urinary system


display: Congenital dislocation of hip, unilateral


display: Congenital dislocation of unspecified hip, unilateral


display: Congenital dislocation of right hip, unilateral


display: Congenital dislocation of left hip, unilateral


display: Congenital dislocation of hip, bilateral


display: Congenital dislocation of hip, unspecified


display: Congenital partial dislocation of hip, unilateral


display: Congenital partial dislocation of unspecified hip, unilateral


display: Congenital partial dislocation of right hip, unilateral


display: Congenital partial dislocation of left hip, unilateral


display: Congenital partial dislocation of hip, bilateral


display: Congenital partial dislocation of hip, unspecified


display: Other specified congenital deformities of hip

names:
Anteversion of femoral neck
Congenital acetabular dysplasia


display: Congenital deformity of hip, unspecified


display: Congenital deformities of feet

excludes1:
reduction defects of feet (Q72.-)
valgus deformities (acquired) (M21.0-)
varus deformities (acquired) (M21.1-)


display: Other congenital varus deformities of feet


display: Congenital pes planus

names:
Congenital flat foot
Congenital rigid flat foot
Congenital spastic (everted) flat foot


display: Other congenital valgus deformities of feet


display: Congenital vertical talus deformity, unspecified foot


display: Congenital vertical talus deformity, right foot


display: Congenital vertical talus deformity, left foot


display: Other specified congenital deformities of feet

names:
Congenital asymmetric talipes
Congenital clubfoot NOS
Congenital talipes NOS
Congenital tarsal coalition
Hammer toe, congenital


display: Congenital deformity of feet, unspecified


display: Congenital musculoskeletal deformities of head, face, spine and chest

excludes1: congenital malformation syndromes classified to Q87.-


display: Other congenital deformities of skull, face and jaw

excludes1: dentofacial anomalies [including malocclusion] (M26.-)

names: Congenital hemifacial atrophy or hypertrophy


display: Congenital deformity of spine

excludes1: scoliosis due to congenital bony malformation (Q76.3)

names:
Congenital postural scoliosis
Congenital scoliosis NOS


display: Other congenital musculoskeletal deformities

excludes2: congenital myotonic chondrodystrophy (G71.13)


display: Congenital deformity of sternocleidomastoid muscle

names: Congenital contracture of sternocleidomastoid (muscle)


display: Congenital deformity of finger(s) and hand

names:
Congenital clubfinger
Spade-like hand (congenital)


display: Congenital deformity of knee

names:
Congenital dislocation of knee
Congenital genu recurvatum


display: Congenital bowing of long bones of leg, unspecified


display: Other specified congenital musculoskeletal deformities

names:
Congenital deformity of clavicle
Congenital deformity of elbow
Congenital deformity of forearm
Congenital deformity of scapula
Congenital deformity of wrist
Congenital dislocation of elbow
Congenital dislocation of shoulder
Congenital dislocation of wrist


display: Fused fingers

names: Complex syndactyly of fingers with synostosis


display: Webbed fingers

names: Simple syndactyly of fingers without synostosis


display: Fused toes

names: Complex syndactyly of toes with synostosis


display: Webbed toes

names: Simple syndactyly of toes without synostosis


display: Polysyndactyly, unspecified

excludes1: specified syndactyly of hand and feet - code to specified conditions (Q70.0- -Q70.3-)


display: Congenital complete absence of upper limb


display: Congenital complete absence of unspecified upper limb


display: Congenital complete absence of right upper limb


display: Congenital complete absence of left upper limb


display: Congenital complete absence of upper limb, bilateral


display: Congenital absence of upper arm and forearm with hand present


display: Congenital absence of unspecified upper arm and forearm with hand present


display: Congenital absence of right upper arm and forearm with hand present


display: Congenital absence of left upper arm and forearm with hand present


display: Congenital absence of upper arm and forearm with hand present, bilateral


display: Congenital absence of both forearm and hand


display: Congenital absence of both forearm and hand, unspecified upper limb


display: Congenital absence of both forearm and hand, right upper limb


display: Congenital absence of both forearm and hand, left upper limb


display: Congenital absence of both forearm and hand, bilateral


display: Congenital absence of unspecified hand and finger


display: Congenital absence of right hand and finger


display: Congenital absence of left hand and finger


display: Congenital absence of hand and finger, bilateral


display: Longitudinal reduction defect of radius

names:
Clubhand (congenital)
Radial clubhand


display: Longitudinal reduction defect of unspecified radius


display: Longitudinal reduction defect of right radius


display: Longitudinal reduction defect of left radius


display: Longitudinal reduction defect of radius, bilateral


display: Longitudinal reduction defect of unspecified ulna


display: Longitudinal reduction defect of right ulna


display: Longitudinal reduction defect of left ulna


display: Longitudinal reduction defect of ulna, bilateral


display: Congenital shortening of right upper limb


display: Congenital shortening of left upper limb


display: Congenital shortening of upper limb, bilateral


display: Congenital shortening of unspecified upper limb


display: Other reduction defects of right upper limb


display: Other reduction defects of left upper limb


display: Other reduction defects of upper limb, bilateral


display: Other reduction defects of unspecified upper limb


display: Unspecified reduction defect of upper limb


display: Unspecified reduction defect of unspecified upper limb


display: Unspecified reduction defect of right upper limb


display: Unspecified reduction defect of left upper limb


display: Unspecified reduction defect of upper limb, bilateral


display: Congenital complete absence of lower limb


display: Congenital complete absence of unspecified lower limb


display: Congenital complete absence of right lower limb


display: Congenital complete absence of left lower limb


display: Congenital complete absence of lower limb, bilateral


display: Congenital absence of thigh and lower leg with foot present


display: Congenital absence of unspecified thigh and lower leg with foot present


display: Congenital absence of right thigh and lower leg with foot present


display: Congenital absence of left thigh and lower leg with foot present


display: Congenital absence of thigh and lower leg with foot present, bilateral


display: Congenital absence of both lower leg and foot


display: Congenital absence of both lower leg and foot, unspecified lower limb


display: Congenital absence of both lower leg and foot, right lower limb


display: Congenital absence of both lower leg and foot, left lower limb


display: Congenital absence of both lower leg and foot, bilateral


display: Congenital absence of unspecified foot and toe(s)


display: Congenital absence of right foot and toe(s)


display: Congenital absence of left foot and toe(s)


display: Congenital absence of foot and toe(s), bilateral


display: Longitudinal reduction defect of unspecified femur


display: Longitudinal reduction defect of right femur


display: Longitudinal reduction defect of left femur


display: Longitudinal reduction defect of femur, bilateral


display: Longitudinal reduction defect of unspecified tibia


display: Longitudinal reduction defect of right tibia


display: Longitudinal reduction defect of left tibia


display: Longitudinal reduction defect of tibia, bilateral


display: Longitudinal reduction defect of unspecified fibula


display: Longitudinal reduction defect of right fibula


display: Longitudinal reduction defect of left fibula


display: Longitudinal reduction defect of fibula, bilateral


display: Congenital shortening of right lower limb


display: Congenital shortening of left lower limb


display: Congenital shortening of lower limb, bilateral


display: Congenital shortening of unspecified lower limb


display: Other reduction defects of right lower limb


display: Other reduction defects of left lower limb


display: Other reduction defects of lower limb, bilateral


display: Other reduction defects of unspecified lower limb


display: Unspecified reduction defect of lower limb


display: Unspecified reduction defect of unspecified lower limb


display: Unspecified reduction defect of right lower limb


display: Unspecified reduction defect of left lower limb


display: Unspecified reduction defect of lower limb, bilateral


display: Congenital absence of unspecified limb(s)


display: Other reduction defects of unspecified limb(s)

names: Longitudinal reduction deformity of unspecified limb(s)


display: Other congenital malformations of limb(s)

excludes1:
polydactyly (Q69.-)
reduction defect of limb (Q71-Q73)
syndactyly (Q70.-)


display: Other congenital malformations of upper limb(s), including shoulder girdle

names:
Accessory carpal bones
Cleidocranial dysostosis
Congenital pseudarthrosis of clavicle
Macrodactylia (fingers)
Madelung's deformity
Radioulnar synostosis
Sprengel's deformity
Triphalangeal thumb


display: Congenital malformation of knee

excludes1:
congenital dislocation of knee (Q68.2)
congenital genu recurvatum (Q68.2)
nail patella syndrome (Q87.2)

names:
Congenital absence of patella
Congenital dislocation of patella
Congenital genu valgum
Congenital genu varum
Rudimentary patella


display: Other congenital malformations of lower limb(s), including pelvic girdle

names: Congenital malformation of sacroiliac joint


display: Other specified congenital malformations of limb(s)


display: Unspecified congenital malformation of limb(s)


display: Other congenital malformations of skull and face bones

excludes1: congenital malformation of face NOS (Q18.-)

excludes1: musculoskeletal deformities of head and face (Q67.0-Q67.4)

excludes1: skull defects associated with congenital anomalies of brain such as:


display: Craniosynostosis

names:
Acrocephaly
Imperfect fusion of skull
Oxycephaly
Trigonocephaly


display: Mandibulofacial dysostosis

names:
Franceschetti syndrome
Treacher Collins syndrome


display: Other specified congenital malformations of skull and face bones

names:
Absence of skull bone, congenital
Congenital deformity of forehead
Platybasia


display: Congenital malformation of skull and face bones, unspecified

names:
Congenital anomaly of face bones NOS
Congenital anomaly of skull NOS


display: Congenital malformations of spine and bony thorax

excludes1: congenital musculoskeletal deformities of spine and chest (Q67.5-Q67.8)


display: Spina bifida occulta

excludes1:
meningocele (spinal) (Q05.-)
spina bifida (aperta) (cystica) (Q05.-)


display: Congenital spondylolisthesis

excludes1:
spondylolisthesis (acquired) (M43.1-)
spondylolysis (acquired) (M43.0-)


display: Congenital scoliosis due to congenital bony malformation

names: Hemivertebra fusion or failure of segmentation with scoliosis


display: Other congenital malformations of spine, not associated with scoliosis


display: Congenital kyphosis, occipito-atlanto-axial region


display: Congenital kyphosis, cervicothoracic region


display: Congenital kyphosis, thoracolumbar region


display: Congenital lordosis, thoracolumbar region


display: Congenital lordosis, sacral and sacrococcygeal region


names: Congenital malformation of lumbosacral (joint) (region) NOS


display: Other congenital malformations of ribs

names:
Accessory rib
Congenital absence of rib
Congenital fusion of ribs
Congenital malformation of ribs NOS


display: Congenital malformation of sternum

names:
Congenital absence of sternum
Sternum bifidum


display: Other congenital malformations of bony thorax


display: Congenital malformation of bony thorax, unspecified


display: Osteochondrodysplasia with defects of growth of tubular bones and spine


display: Chondrodysplasia punctata

excludes1: Rhizomelic chondrodysplasia punctata (E71.43)


display: Other osteochondrodysplasia with defects of growth of tubular bones and spine


display: Osteochondrodysplasia with defects of growth of tubular bones and spine, unspecified


display: Other osteochondrodysplasias


display: Osteogenesis imperfecta

names:
Fragilitas ossium
Osteopsathyrosis


display: Osteopetrosis

names:
Albers-Schönberg syndrome
Osteosclerosis NOS


display: Enchondromatosis

names:
Maffucci's syndrome
Ollier's disease


display: Osteochondrodysplasia, unspecified

names:
Chondrodystrophy NOS
Osteodystrophy NOS


display: Congenital malformations of musculoskeletal system, not elsewhere classified

excludes2: congenital (sternomastoid) torticollis (Q68.0)


display: Other congenital malformations of diaphragm

names: Congenital malformation of diaphragm NOS


display: Prune belly syndrome

names:
Congenital prolapse of bladder mucosa
Eagle-Barrett syndrome


display: Other congenital malformations of abdominal wall


display: Other congenital malformations of musculoskeletal system

names:
Absence of muscle
Absence of tendon
Accessory muscle
Amyotrophia congenita
Congenital constricting bands
Congenital shortening of tendon
Poland syndrome


display: Congenital malformation of musculoskeletal system, unspecified

names: Congenital anomaly of musculoskeletal system NOS

names: Congenital deformity of musculoskeletal system NOS


display: Congenital bullous ichthyosiform erythroderma


display: Other congenital malformations of skin

excludes1: congenital erythropoietic porphyria (E80.0)

excludes1: Sturge-Weber (-Dimitri) syndrome (Q85.8)


display: Congenital cutaneous mastocytosis

excludes1: diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)

excludes1: urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

names: Congenital diffuse cutaneous mastocytosis

names: Congenital maculopapular cutaneous mastocytosis


display: Congenital non-neoplastic nevus

excludes2:
Café au lait spots (L81.3)
lentigo (L81.4)
nevus NOS (D22.-)
araneus nevus (I78.1)
melanocytic nevus (D22.-)
pigmented nevus (D22.-)
spider nevus (I78.1)
stellar nevus (I78.1)

names:
Birthmark NOS
Flammeus Nevus
Portwine Nevus
Sanguineous Nevus
Strawberry Nevus
Vascular Nevus NOS
Verrucous Nevus


display: Congenital sacral dimple

excludes2:
pilonidal cyst with abscess (L05.01)
pilonidal cyst without abscess (L05.91)


display: Other specified congenital malformations of skin

names: Benign familial pemphigus [Hailey-Hailey]

names: Inherited keratosis palmaris et plantaris


display: Congenital malformation of skin, unspecified


display: Congenital malformations of breast

excludes2:
absence of pectoral muscle (Q79.8)
hypoplasia of breast (N64.82)
micromastia (N64.82)


display: Congenital absence of breast with absent nipple


display: Other congenital malformations of breast


display: Congenital malformation of breast, unspecified


display: Other congenital malformations of integument